Liver lymphangioma, a rare tumor originating from the lymphatic system, typically affects the liver partially and is usually found in the neck and armpits. The etiology is unclear but is thought to result from congenital malformations of hepatic lymphatic vessels. Pathologically, liver lymphangiomas are characterized by cystic solid lesions in the liver parenchyma, containing serous and chylous fluid. Lesions often show immunohistochemical markers such as CD31, CD34, and FV III. Clinically, patients may experience upper abdominal discomfort or acute abdominal pain. Laboratory tests often show negative tumor markers, with mild liver function abnormalities in some cases. Imaging typically reveals cystic and solid components with heterogeneous septal thickness, visible on MRI as low signals on T1WI and high signals on T2WI. Differential diagnosis includes liver hemangioma, vascular lymphangioma, mesenchymal hamartoma, cystadenoma, cystadenocarcinoma, and giant liver cysts, with pathological diagnosis being the gold standard. A case study of a liver lymphangioma will be briefly introduced.