Intraocular structures of the eye are known to have specialized specific function. Tumors arising from each of this individual structure has unique histomorphological architecture. Immunohistochemical staining corroborates the histomorphological diagnosis. Recent technical advances in the diagnostic tools have increased the precision of intraocular tumor diagnosis. Most often clinical and radiological correlation clinches the diagnosis in most of the cases however, histomorphology provides the accurate diagnosis. Tumors are broadly classified into benign and malignant. The tumors arising from uveal tissue are mostly pigmented melanomas and are classified based on the cellular shape. Choroidal melanomas are more common than Iris or Ciliary body melanomas. Amelanotic melanomas are also noted. Retinoblastoma is more common in children of developing countries and is classified based on the percentage presence of rosettes. The presence of histopathological high-risk features determines the administration of adjuvant systemic chemotherapy. Ciliary body tumors are rare but most often cause neovascular glaucoma. Tumors arising from ciliary body are adenocarcinomas or adenomas. Lymphomas are mostly B-cell lymphomas and tend to involve CNS. Choroidal metastases are the most common intraocular tumors. Vascular lesions are often misdiagnosed as choroidal melanomas and tend to have syndromic associations. Optic disc tumors are rare.