Anesthetic Management of Cardiac Catheterization in Children with Dilated Cardiomyopathy and Pulmonary Arterial Hypertension
摘要
A 4-year-old girl was diagnosed with incomplete myocardial densification and pulmonary arterial hypertension (PAH) at a local hospital 3 years ago, which was not alleviated by treatment with internal medicines. She was diagnosed with dilated cardiomyopathy (DCM) and severe PAH at our hospital 8 months ago. Targeted drugs, including tadalafil and bosentan treated the PAH. Metoprolol was used to control heart rate. Furosemide and spironolactone were used for symptomatic treatments. Recently, she experienced recurrent syncope with the New York Heart Association (NYHA) classification of heart failure class III. She was scheduled to undergo cardiac catheterization under general anesthesia. The key point of anesthetic management is to maintain heart function and avoid the increase of pulmonary vascular resistance.