Congenital vascular malformations (VM) encompass a wide spectrum of lesions with varying degrees of severity. The confusing terminology in the literature has led to the developpement of many classifications systems. The International Society for the Study of Vascular Anomalies (ISSVA) classification is the mostly accepted and has been recently updated. In Africa in general and subsaharan Africa in particular, very few reports have been written using those confusing terminologies thereby leading to poor description of the lesions. The aim of our study is to describe the patients characteristic and pattern of VM in Tropical Africa in General and Yaounde in particular outlining the importance of accurate description of the lesions in light of the current concepts, classifications and terminology. All the patients diagnosed of VM during a 10 years period (january 2007 to october 2016) are included. For each patient clinical examination, duplex ultrasound and if necessary X-rays, Computer tomography, MRI were performed. The following data were retrieved:epidemiological data, description of the malformation (the symptoms, the type, the location, the extend, the sizes), the presence of an associated non vascular malformation. During the study period, 51 VM were diagnosed in 47 patients. The age was 2 weeks to 29 years. Thirty six (76.59%) were male and 15 (23.40) female. As far as the type of VM is concerned, the venous malformations were the most common followed by capillary and combined. Two truncular aortic malformation were seen. It was noticed that 8 of the 9 combined VM-syndromes (8 Klippel-Trenaunay syndrome and 1 Parkes-Weber syndrome) were found in male patients. The sizes of the VM ranged from spotlike lesion to extensive lesion and huge mass. With regards to the location of the VM, the limbs were found to be most affected (58.82%) with the lower limbs being more affected than the upper limbs.

错误:搜索内容不能为空,请输入英文关键词
错误:关键词超出字数限制,请精简
高级检索

Pattern of Vascular Malformations in a Sub-Saharan Africa Setting

  • Marcus Fokou,
  • Abel Teyang,
  • Emmanuel Fongang

摘要

Congenital vascular malformations (VM) encompass a wide spectrum of lesions with varying degrees of severity. The confusing terminology in the literature has led to the developpement of many classifications systems. The International Society for the Study of Vascular Anomalies (ISSVA) classification is the mostly accepted and has been recently updated. In Africa in general and subsaharan Africa in particular, very few reports have been written using those confusing terminologies thereby leading to poor description of the lesions. The aim of our study is to describe the patients characteristic and pattern of VM in Tropical Africa in General and Yaounde in particular outlining the importance of accurate description of the lesions in light of the current concepts, classifications and terminology. All the patients diagnosed of VM during a 10 years period (january 2007 to october 2016) are included. For each patient clinical examination, duplex ultrasound and if necessary X-rays, Computer tomography, MRI were performed. The following data were retrieved:epidemiological data, description of the malformation (the symptoms, the type, the location, the extend, the sizes), the presence of an associated non vascular malformation. During the study period, 51 VM were diagnosed in 47 patients. The age was 2 weeks to 29 years. Thirty six (76.59%) were male and 15 (23.40) female. As far as the type of VM is concerned, the venous malformations were the most common followed by capillary and combined. Two truncular aortic malformation were seen. It was noticed that 8 of the 9 combined VM-syndromes (8 Klippel-Trenaunay syndrome and 1 Parkes-Weber syndrome) were found in male patients. The sizes of the VM ranged from spotlike lesion to extensive lesion and huge mass. With regards to the location of the VM, the limbs were found to be most affected (58.82%) with the lower limbs being more affected than the upper limbs.