Uveal vascular tumors represent benign hamartomatous disorders and are classified as hemangiomas. Although the iris and ciliary body can be involved, hemangiomas most frequently affect the choroid. Choroidal hemangioma can either be circumscribed or diffuse. In general, uveal hemangioma may be confined to the globe or be a manifestation of a widespread hemangiomatous disorder. Iris vascular anomalies can be classified into five distinct clinicopathological entities: capillary hemangioma, iris cavernous hemangioma, iris microhemangioma, iris arteriovenous malformation, and iris varix. Only a few cases of well-documented ciliary body hemangioma have been published. Circumscribed choroidal hemangioma is usually diagnosed between the second and fourth decade of life when it causes visual disturbances due to the development of exudative retinal detachment or macular edema. In contrast, diffuse choroidal hemangioma is usually evident at birth and generally occurs as a part of neuro-oculo-cutaneous hemangiomatosis (Sturge-Weber syndrome).