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<p>Congenital aortopulmonary window (APW) associated with interrupted aortic arch (IAA) is a rare and severe form of congenital heart disease. The optimal surgical timing and strategy remain challenging, particularly beyond infancy. We report two toddlers diagnosed with APW and IAA who underwent one-stage surgical repair. At the time of surgery, the children were 17 and 22 months old, with body weights of 6.6&#xa0;kg and 8.0&#xa0;kg, respectively. Both patients survived and experienced no perioperative complications. During postoperative follow-up of 12 and 19 months, respectively, the children demonstrated New York Heart Association (NYHA) class I cardiac function, with normal intracardiac anatomy and no evidence of residual shunting, vascular stenosis, or pulmonary hypertension. These cases indicate that delayed one-stage repair beyond infancy can be performed safely and effectively in selected patients with preoperative evaluation and individualized surgical planning.</p>

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Single-stage surgical repair of congenital aortopulmonary window associated with interrupted aortic arch in two toddlers: a case report

  • 期刊论文

  • 出版模式：

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  • 发表日期：

    2026年7月17日

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  • Junxiang Pan,
  • Mengqi Zhao,
  • Xiaoya Zhang,
  • Enrui Zhang,
  • Yongqiang Jin

摘要

Congenital aortopulmonary window (APW) associated with interrupted aortic arch (IAA) is a rare and severe form of congenital heart disease. The optimal surgical timing and strategy remain challenging, particularly beyond infancy. We report two toddlers diagnosed with APW and IAA who underwent one-stage surgical repair. At the time of surgery, the children were 17 and 22 months old, with body weights of 6.6 kg and 8.0 kg, respectively. Both patients survived and experienced no perioperative complications. During postoperative follow-up of 12 and 19 months, respectively, the children demonstrated New York Heart Association (NYHA) class I cardiac function, with normal intracardiac anatomy and no evidence of residual shunting, vascular stenosis, or pulmonary hypertension. These cases indicate that delayed one-stage repair beyond infancy can be performed safely and effectively in selected patients with preoperative evaluation and individualized surgical planning.