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Objectives <p>Congenital pulmonary airway malformation (CPAM) lesion with an aberrant systemic blood supply is considered a “hybrid” lesion (HL). The aim of the study was to report authors’ experience in the presentation, surgical management, and outcomes of HL.</p> Methods <p>A retrospective cohort study of HL patients followed from 2000 to 2022 in a single institution was done. Clinical and radiographic data were collected from the medical records.</p> Results <p>Over the study period, 39 patients with HL were identified. HL with CPAM type 2 was more common than type 1 (74% vs. 26%), and intralobar sequestrations were more prevalent than extralobar sequestrations (ELS) (79.5% vs. 20.5%). HL with CPAM type 2 had higher rates of co-morbidities and higher likelihood to present with respiratory symptoms after birth. HL with ELS had smaller feeding vessels (all &lt; 4&#xa0;mm) which resulted in lower rates of open thoracotomy approach for resection.</p> Conclusions <p>The variability in HL patient presentation and outcomes is correlated with the size and the hybrid composition.&#xa0;</p>

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Congenital Pulmonary Hybrid Lesions: Clinical Presentation, Surgical Management, and Outcomes

  • 期刊论文

  • 发表日期：

    2025年1月21日

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  • Dvir Gatt,
  • Eveline Lapidus-Krol,
  • Priscilla P. L. Chiu

摘要

Objectives

Congenital pulmonary airway malformation (CPAM) lesion with an aberrant systemic blood supply is considered a “hybrid” lesion (HL). The aim of the study was to report authors’ experience in the presentation, surgical management, and outcomes of HL.

Methods

A retrospective cohort study of HL patients followed from 2000 to 2022 in a single institution was done. Clinical and radiographic data were collected from the medical records.

Results

Over the study period, 39 patients with HL were identified. HL with CPAM type 2 was more common than type 1 (74% vs. 26%), and intralobar sequestrations were more prevalent than extralobar sequestrations (ELS) (79.5% vs. 20.5%). HL with CPAM type 2 had higher rates of co-morbidities and higher likelihood to present with respiratory symptoms after birth. HL with ELS had smaller feeding vessels (all < 4 mm) which resulted in lower rates of open thoracotomy approach for resection.

Conclusions

The variability in HL patient presentation and outcomes is correlated with the size and the hybrid composition.