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<p>Kaposiform hemangioendothelioma (KHE) is a rare aggressive vascular tumour of intermediate malignant potential and often associated with thrombocytopaenia, known as the Kasabach–Merritt phenomenon (KMP). Herein, we report a case of a 3-month-old child with a left neck mass, subsequently diagnosed with KHE, complicated with KMP. This case was managed with a multidisciplinary team involvement and successfully treated with the combination of steroids and sirolimus. As the diagnosis of KHE itself is rare, one may miss the differential diagnosis causing a delay in referral and subsequently late in diagnosis and initiating the treatment.</p>

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Kaposiform Hemangioendothelioma with Kasabach-Merritt Phenomenon: A Rare Diagnosis of Neck Mass in a Child

  • 期刊论文

  • 发表日期：

    2025年6月4日

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  • Anis Che Mohd Amin,
  • Najwa Raihan Zulkiflee,
  • Azliana Aziz,
  • Hashimah Ismail

摘要

Kaposiform hemangioendothelioma (KHE) is a rare aggressive vascular tumour of intermediate malignant potential and often associated with thrombocytopaenia, known as the Kasabach–Merritt phenomenon (KMP). Herein, we report a case of a 3-month-old child with a left neck mass, subsequently diagnosed with KHE, complicated with KMP. This case was managed with a multidisciplinary team involvement and successfully treated with the combination of steroids and sirolimus. As the diagnosis of KHE itself is rare, one may miss the differential diagnosis causing a delay in referral and subsequently late in diagnosis and initiating the treatment.