Purpose of this review <p>Behçet's syndrome (BS) frequently comes up in the differential diagnosis of many conditions, including but not limited to rheumatological, dermatological, ophthalmological, neurological and gastrointestinal diseases. We present here a summary of what is currently known about this condition and recent published literature that may help in the diagnosis and management of BS patients.</p> Recent findings <p>A better understanding of the pathogenesis of BS may help potentially better treatment options to be developed. New epidemiological studies have shown that BS may not be as rare in certain areas as previously thought. New treatment options and clinical trials are providing both patients and doctors treating BS with more options and potentially better outcomes. New imaging modalities are helping the diagnosis and monitoring of BS patients.</p> Summary <p>Better understanding of pathogenesis and availability of treatment options are helping improve outcomes in BS patients.</p>