Scholarlink

<p>Rosai-Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a rare histiocytic disorder characterized by proliferation of non-Langerhans cell phagocytic histiocytes. Most patients present with painless massive cervical lymphadenopathy with associated night sweats, malaise, and fever. Osseous manifestations of RDD are uncommon and primary RDD of the bone without lymphadenopathy is thought to be even rarer. It is important to maintain this entity on a differential as it can mimic an aggressive entity. This is exemplified in our case report of a 24-year-old female patient with an incidental finding of a nonspecific mass in the right hemipelvis which was determined to be isolated osseous Rosai-Dorfman disease after a multidisciplinary investigation.</p>

错误：搜索内容不能为空，请输入英文关键词
错误：关键词超出字数限制，请精简
高级检索

Isolated osseous Rosai-Dorfman disease: a case report and review of literature

  • 期刊论文

  • 出版模式：

    开放获取

  • 发表日期：

    2025年7月28日

查看全文
  • Justin J. Sun,
  • Benjamin Emert,
  • Sarah Dry,
  • Fatemeh Abdollahi Mofakham

摘要

Rosai-Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a rare histiocytic disorder characterized by proliferation of non-Langerhans cell phagocytic histiocytes. Most patients present with painless massive cervical lymphadenopathy with associated night sweats, malaise, and fever. Osseous manifestations of RDD are uncommon and primary RDD of the bone without lymphadenopathy is thought to be even rarer. It is important to maintain this entity on a differential as it can mimic an aggressive entity. This is exemplified in our case report of a 24-year-old female patient with an incidental finding of a nonspecific mass in the right hemipelvis which was determined to be isolated osseous Rosai-Dorfman disease after a multidisciplinary investigation.